Congenital smooth muscle hamartoma

A one-year-old Japanese boy presented with brown macules on the waist.

 

Diagnosis: 
Congenital smooth muscle hamartoma
Comment: 

This lesion showed a positive pseudo-Darier sign (which is a transient piloerection and elevation of a lesion induced by rubbing and is observed especially in congenital smooth muscle hamartomas)

Immunohistochemical staining for α-SMA was positive in the tumor cells.

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