Article Contributors:
Sean Klepper M.D.
Stephen Lyle, M.D., ...
Clinical Features:
- Familial photodermatosis of unknown etiology, most often affecting Native Americans
- Most commonly presents on the face with coarsening of facial features
- There is often an associated cheilitis, called follicular cheilitis or actinic prurigo cheilitis.
Histologic Features:
- Acute lesions (indistinguishable from polymorphous light eruption):
- Superficial dermal perivascular lymphocytic infiltrate
- Chronic lesions:
- Hyperkeratosis
- Acanthosis
- Signs of photoadaptation
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