- Erythematous plaques devoid of hair, most commonly on the head and neck
- Most often self-limiting
- 30% of cases are associated with a lymphoproliferative disorder, especially a cutaneous T-cell lymphoma.
- Follicular mucinosis (deposition of mucin within the follicular epithelium) beginning in the infundibulum and eventually involving the entire follicle with formation of mucin-filled cystic spaces
- Perifollicular infiltration of lymphocytes with some eosinophils