Clinical Features:

• Disease may be limited to the skin, or it may be a manifestation of systemic disease.
• Presents with indurated erythematous or violaceous patches or plaques
• Commonly affects the trunk and thighs

Histologic Features:

• Large atypical lymphocytes, often with prominent nucleoli, filling distended blood vessels within the dermis and subcutis
• The neoplastic lymphocytes are positive for pan-B-cell markers.
• CD5 is sometimes positive.
• A rare T-cell variant has also been described.