Also known as: localized scleroderma, circumscribed scleroderma
- Represents a localized form of scleroderma
- Patients may rarely go on to develop systemic scleroderma.
- Most common in young to middle-aged women
- Controversial relationship with Borrelia burgdoferi
- Presents as indurated whitish plaques with a peripheral "lilac ring" rim.
- Early lesions:
- Sclerosis of the reticular dermis
- Superficial and deep perivascular lymphocytic infiltrate
- Later lesions:
- Increasing sclerosis of the dermis with hyalinization and extension of the sclerosis into the subcutaneous fat
- Atrophy and dropout of adnexal structures with "entrapment" of eccrine glands between sclerotic collagen bundles
- Sometimes nodular collections of lymphocytes at the the dermal-subcutaneous junction
- The epidermis is normal or atrophic.