- Benign lesion, most commonly seen on the fingers and palms of young adults
- Well-circumscribed lesion in the dermis and/or subcutis
- Composed of hyalinized collagen with interspersed bland spindle cells, arranged in cords, bundles and whorls
- Immunohistochemically, the tumor cells are positive for EMA and negative for S-100. Some cases are focally positive for CD34.