- Solitary skin-colored nodule
- Cured by simple excision
- Multiple lesions may be seen in Cowden's disease, where they may occur in the oral cavity.
- Well-circumscribed dermal lesion
- Composed of bundles of hyalinized collagen bundles in a storiform pattern, separated by clefts
- Spindle cells are interspersed between the collagen bundles.
- Giant cell collagenoma is a variant that contains scattered multinucleated giant cells, which may have a bizarre appearance.