- Most likely a malformation rather than a neoplasm
- Most common on the upper face and genital region
- Usually multifocal
- Usually present as small white to yellow papules
- Several variants have been described.
- Well-defined lesion consisting of comma-shaped groups of epithelial cells with tubule formation and focal formation of lumina lined by cuticles
- The cells are polygonal to flattened with eosinophilic to clear cytoplasm and bland nuclei without mitoses